Cardiac hydatidosis is a rare but potentially life-threatening infestation. Cardiac hydatid cysts generally occur in the left ventricle; followed by the atria, the free wall of the right ventricle, the pericardium and the interventricular septum. Herein, we report a 17-year-old girl with a giant left ventricle cyst who was previously treated by interventional methods for liver and lung hydatid cysts. The cardiac cyst was removed with cardiopulmonary bypass support.