Invasive fungal infections cause significant morbidity and mortality in pediatric cancer patients. Candida species are the most frequently isolated pathogen. Candida species may cause bloodstream and deep-seated infection in neutropenic children with cancer. The gastrointestinal system, lung, liver and spleen are the most frequently involved organs. Isolated renal involvement presented as abscess formation has been reported rarely in children with cancer. Herein, we report a patient with acute lymphoblastic leukemia (ALL) who presented with renal abscess and fungus ball formation due to Candida norvegensis, which is an unusual cause of infection.