Congenital lobar emphysema is cause of infantile respiratory distress and diagnosed by lobar overaeration, mediastinal shift and/or compression of the adjacent lobe. However, concomitant congenital heart disease with this clinical condition is not uncommon, and there is no uniform consensus about the treatment strategy in these particular cases. We present a child who was treated with division of large patent ductus arteriosus without the lobectomy.