A ten-month-old boy was admitted to our hospital with fever, cough and dyspnea. His history was remarkable for mild respiratory problems from the early neonatal period. Although medical treatment was administered several times in a local hospital, his symptoms recurred. Chest x-ray revealed multiple cystic lesions on the right side. The diagnosis of congenital cystic disease was considered preoperatively, to our knowledge for the first time in our hospital. The patient's postoperative course was uneventful, and no respiratory problems have recurred in 24 months of follow-up.