Abstract

A four-year-old-girl with hyper-IgE syndrome is presented. She had a coarse facial appearance, pruritic dermatitis, recurrent skin abscesses, pulmonary infection, spontaneous bone fractures, and an elevated serum IgE concentration. She has been treated with cimetidine, ascorbic acid and trimethoprim-sulfamethoxazole for the last two years and there has been no evidence of a severe infection.

Keywords: hyper-IgE syndrome, bone fractures, cimetidine, vitamin C

How to cite

1.
Sanal Ö, Göçmen A, Tezcan İ, Ersoy F, Adalıoğlu G. Hyper-IgE syndrome: a case report. Turk J Pediatr 1990; 32: 273-278. https://doi.org/10.24953/turkjpediatr.1990.3819