The May-Hegglin anomaly is a rare autosomal dominant disorder characterized by the presence of large, bizarre, cigar-shaped platelets and Döhle bodies in the leukocytes. This rare anomaly was detected in seven members of a family. It is emphasized that in making a differential diagnosis this disorder must be distinguished from the other mild bleeding disorders.

Keywords: May-Hegglin anomaly, mild-bleeding disorder, Döhle body