Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a clinical entity characterized by myocardial necrosis which becomes symptomatic shortly after birth; survival beyond infancy is uncommon because of severe left heart failure. To our knowledge, it is rare for an ALCAPA patient to survive to adulthood. Here we present a case of a 17-year-old girl with ALCAPA who was referred to our hospital because of palpitation and dyspnea.