Abstract
Two patients with hepatic glycogenosis associated with Fanconi syndrome are presented. Both patients were treated with a neutral phosphorus solution, an oral alkaline solution, cholecalciferol and uncooked cornstarch. The proximal renal tubular functions were corrected in the patient who used cornstarch properly, which may indicate a causal relationship between Fanconi syndrome and glycogenosis.
Copyright and license
Copyright © 1993 The Author(s). This is an open access article distributed under the Creative Commons Attribution License (CC BY), which permits unrestricted use, distribution, and reproduction in any medium or format, provided the original work is properly cited.
How to cite
1.
Yüce A, Coşkun T, Koçak N, Ozsoylu S, Ozalp I, Göğüş S. Type I glycogenosis with renal tubular dysfunction (presentation of two cases). Turk J Pediatr 1993; 35: 201-204.
