Abstract
The normal biosynthetic pathway of porphyrins and their metabolic turnover are reviewed. The chemical findings in various forms of porphyria are presented and the biochemical defects and mechanism that may lead to the observed biochemical pathology are outlined.
Copyright and license
Copyright © 1962 The Author(s). This is an open access article distributed under the Creative Commons Attribution License (CC BY), which permits unrestricted use, distribution, and reproduction in any medium or format, provided the original work is properly cited.
How to cite
1.
Özand PT. Biochemical pathology in porphyrin metabolism. Turk J Pediatr 1962; 4: 225-245. https://doi.org/10.24953/turkjpediatr.1962.9281