Mucormycosis of the intestine is a rare fungal infection of childhood and is mostly encountered in neonates. It is a potentially lethal opportunistic fungal infection with rapid progression and high mortality in immunocompromised patients. The number of reported cases with intestinal mucormycosis is 19 to date. We herein report an asphyxiated preterm infant with intestinal mucormycosis who was presented with an atypical necrotizing enterocolitis (NEC), with findings similar to an intraabdominal mass. The diagnosis was made in the postmortem examination of the surgically removed bowel segment. Prematurity and asphyxia are important risk factors for mucormycosis. We suggest that the diagnosis of gastrointestinal mucormycosis should be considered in the differential diagnosis of atypical NEC cases.